D66

Hereditary factor VIII deficiency

Risk-adjusting (HCC)Billable code

HCC risk adjustment mapping

CMS-HCC V28

HCC111

Hemophilia, Male

CMS-HCC ESRD V24

HCC46

Severe Hematological Disorders

Coding notes

Excludes 1 never coded together · Excludes 2 may co-exist

This code · D66
Excludes 1

factor VIII deficiency with vascular defect (D68.0-)

Synonyms

Classical hemophilia Deficiency factor VIII (with functional defect) Hemophilia NOS Hemophilia A

Inherited from chapter 3Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Excludes 2

autoimmune disease (systemic) NOS (M35.9) certain conditions originating in the perinatal period (P00-P96) complications of pregnancy, childbirth and the puerperium (O00-O9A) congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) endocrine, nutritional and metabolic diseases (E00-E88) human immunodeficiency virus [HIV] disease (B20) injury, poisoning and certain other consequences of external causes (S00-T88) neoplasms (C00-D49) symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Official Guidelines for D66

FY 2026 ›