D68.2

Hereditary deficiency of other clotting factors

Risk-adjusting (HCC)Billable code

HCC risk adjustment mapping

CMS-HCC V28

HCC112

Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions

CMS-HCC ESRD V24

HCC48

Coagulation Defects and Other Specified Hematological Disorders

Coding notes

Excludes 1 never coded together · Excludes 2 may co-exist

This code · D68.2
Synonyms

AC globulin deficiency Congenital afibrinogenemia Deficiency of factor I [fibrinogen] Deficiency of factor II [prothrombin] Deficiency of factor V [labile] Deficiency of factor VII [stable] Deficiency of factor X [Stuart-Prower] Deficiency of factor XII [Hageman] Deficiency of factor XIII [fibrin stabilizing] Dysfibrinogenemia (congenital) Hypoproconvertinemia Owren's disease Proaccelerin deficiency

Inherited from D68Other coagulation defects
Excludes 1

abnormal coagulation profile NOS (R79.1)

Excludes 2

coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1) coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

Inherited from chapter 3Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Excludes 2

autoimmune disease (systemic) NOS (M35.9) certain conditions originating in the perinatal period (P00-P96) complications of pregnancy, childbirth and the puerperium (O00-O9A) congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) endocrine, nutritional and metabolic diseases (E00-E88) human immunodeficiency virus [HIV] disease (B20) injury, poisoning and certain other consequences of external causes (S00-T88) neoplasms (C00-D49) symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Official Guidelines for D68.2

FY 2026 ›