D74.0
Congenital methemoglobinemia
This code does not map to a risk-adjusting HCC in the loaded models.
Coding notes
Excludes 1 never coded together · Excludes 2 may co-exist
Congenital NADH-methemoglobin reductase deficiency Hemoglobin-M [Hb-M] disease Methemoglobinemia, hereditary
autoimmune disease (systemic) NOS (M35.9) certain conditions originating in the perinatal period (P00-P96) complications of pregnancy, childbirth and the puerperium (O00-O9A) congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) endocrine, nutritional and metabolic diseases (E00-E88) human immunodeficiency virus [HIV] disease (B20) injury, poisoning and certain other consequences of external causes (S00-T88) neoplasms (C00-D49) symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Official Guidelines for D74.0
FY 2026 ›Find D74.0 in the alphabetic index
8 index paths lead to this code
- Deficiency, deficient › NADH diaphorase or reductase
- Deficiency, deficient › NADH-methemoglobin reductase
- Disease, diseased › diaphorase deficiency
- Methemoglobinemia › congenital
- Methemoglobinemia › enzymatic
- Methemoglobinemia › Hb M disease
- Methemoglobinemia › hereditary
- Disease, diseased › hemoglobin or Hb › M