D76.3
Other histiocytosis syndromes
HCC risk adjustment mapping
CMS-HCC V28
Specified Immunodeficiencies and White Blood Cell Disorders
CMS-HCC ESRD V24
Disorders of Immunity
Coding notes
Excludes 1 never coded together · Excludes 2 may co-exist
Reticulohistiocytoma (giant-cell) Sinus histiocytosis with massive lymphadenopathy Xanthogranuloma
(Abt-) Letterer-Siwe disease (C96.0) eosinophilic granuloma (C96.6) Hand-Schüller-Christian disease (C96.5) histiocytic medullary reticulosis (C96.9) histiocytic sarcoma (C96.A) histiocytosis X, multifocal (C96.5) histiocytosis X, unifocal (C96.6) Langerhans-cell histiocytosis, multifocal (C96.5) Langerhans-cell histiocytosis NOS (C96.6) Langerhans-cell histiocytosis, unifocal (C96.6) leukemic reticuloendotheliosis (C91.4-) lipomelanotic reticulosis (I89.8) malignant histiocytosis (C96.A) malignant reticulosis (C86.0) nonlipid reticuloendotheliosis (C96.0)
autoimmune disease (systemic) NOS (M35.9) certain conditions originating in the perinatal period (P00-P96) complications of pregnancy, childbirth and the puerperium (O00-O9A) congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) endocrine, nutritional and metabolic diseases (E00-E88) human immunodeficiency virus [HIV] disease (B20) injury, poisoning and certain other consequences of external causes (S00-T88) neoplasms (C00-D49) symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Official Guidelines for D76.3
FY 2026 ›Find D76.3 in the alphabetic index
12 index paths lead to this code
- Histiocytosis
- Reticulohistiocytoma
- Xanthogranuloma
- Granuloma › reticulohistiocytic
- Histiocytosis › lipid, lipoid
- Histiocytosis › non-Langerhans cell
- Histiocytosis › polyostotic sclerosing
- Histiocytosis › sinus, with massive lymphadenopathy
- Histiocytosis › syndrome NEC
- Lipoid › histiocytosis
- Syndrome › histiocytic
- Syndrome › histiocytosis NEC