D80.1
Nonfamilial hypogammaglobulinemia
HCC risk adjustment mapping
CMS-HCC ESRD V24
Disorders of Immunity
RxHCC V08
Immune Disorders
Coding notes
Excludes 1 never coded together · Excludes 2 may co-exist
Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes Common variable agammaglobulinemia [CVAgamma] Hypogammaglobulinemia NOS
autoimmune disease (systemic) NOS (M35.9) certain conditions originating in the perinatal period (P00-P96) complications of pregnancy, childbirth and the puerperium (O00-O9A) congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) endocrine, nutritional and metabolic diseases (E00-E88) human immunodeficiency virus [HIV] disease (B20) injury, poisoning and certain other consequences of external causes (S00-T88) neoplasms (C00-D49) symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Official Guidelines for D80.1
FY 2026 ›Find D80.1 in the alphabetic index
11 index paths lead to this code
- Agammaglobulinemia
- Hypogammaglobulinemia
- Absence › gamma globulin in blood
- Agammaglobulinemia › common variable
- Deficiency, deficient › gammaglobulin in blood
- Hypogammaglobulinemia › nonfamilial
- Agammaglobulinemia › with › immunoglobulin-bearing B-lymphocytes
- Arthritis, arthritic › in › hypogammaglobulinemia
- Syndrome › antibody deficiency › agammaglobulinemic
- Syndrome › antibody deficiency › hypogammaglobulinemic
- Disease, diseased › connective tissue, systemic › in › hypogammaglobulinemia