D84.1
Defects in the complement system
HCC risk adjustment mapping
CMS-HCC V28
Specified Immunodeficiencies and White Blood Cell Disorders
CMS-HCC ESRD V24
Other Significant Endocrine and Metabolic Disorders
RxHCC V08
Hereditary Angioedema and Other Defects in the Complement System
Coding notes
Excludes 1 never coded together · Excludes 2 may co-exist
C1 esterase inhibitor [C1-INH] deficiency
autoimmune disease (systemic) NOS (M35.9) certain conditions originating in the perinatal period (P00-P96) complications of pregnancy, childbirth and the puerperium (O00-O9A) congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) endocrine, nutritional and metabolic diseases (E00-E88) human immunodeficiency virus [HIV] disease (B20) injury, poisoning and certain other consequences of external causes (S00-T88) neoplasms (C00-D49) symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Official Guidelines for D84.1
FY 2026 ›Find D84.1 in the alphabetic index
16 index paths lead to this code
- Angioedema › hereditary
- Angioneurotic edema › hereditary
- Bannister's disease › hereditary
- Defect, defective › complement system
- Deficiency, deficient › C1 esterase inhibitor
- Quincke's disease or edema › hereditary
- Edema, edematous › angioneurotic › hereditary
- Edema, edematous › circumscribed, acute › hereditary
- Edema, edematous › essential, acute › hereditary
- Edema, edematous › periodic › hereditary
- Edema, edematous › Quincke's › hereditary
- Giant › urticaria › hereditary
- Urticaria › with angioneurotic edema › hereditary
- Urticaria › giant › hereditary
- Urticaria › larynx › hereditary
- Edema, edematous › glottis, glottic, glottidis › allergic › hereditary