E71.19
Other disorders of branched-chain amino-acid metabolism
HCC risk adjustment mapping
CMS-HCC ESRD V24
Other Significant Endocrine and Metabolic Disorders
RxHCC V08
Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
Coding notes
Excludes 1 never coded together · Excludes 2 may co-exist
Hyperleucine-isoleucinemia Hypervalinemia
transitory endocrine and metabolic disorders specific to newborn (P70-P74)
All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Official Guidelines for E71.19
FY 2026 ›Find E71.19 in the alphabetic index
13 index paths lead to this code
- Hyperleucine-isoleucinemia
- Hypervalinemia
- Isoleucinosis
- Disorder › hyperleucine-isoleucinemia
- Disorder › hypervalinemia
- Hypoglycemia › leucine-induced
- Disorder › branched-chain amino-acid metabolism › specified NEC
- Disorder › metabolism NOS › isoleucine
- Disorder › metabolism NOS › leucine
- Disorder › metabolism NOS › valine
- Disorder › metabolism NOS › amino-acid › branched chain › hyperleucine-isoleucinemia
- Disorder › metabolism NOS › amino-acid › branched chain › hypervalinemia
- Disorder › metabolism NOS › amino-acid › branched chain › other specified