E75.4

Neuronal ceroid lipofuscinosis

Risk-adjusting (HCC)Billable code

HCC risk adjustment mapping

CMS-HCC ESRD V24

HCC52

Dementia Without Complication

RxHCC V08

RXHCC41

Lysosomal Storage Disorders

Coding notes

Excludes 1 never coded together · Excludes 2 may co-exist

This code · E75.4

Synonyms

Batten disease Bielschowsky-Jansky disease Kufs disease Spielmeyer-Vogt disease

Inherited from E75Disord of sphingolipid metab and oth lipid storage disorders

Excludes 1

mucolipidosis, types I-III (E77.0-E77.1) Refsum's disease (G60.1)

Inherited from E70-E88Metabolic disorders

Excludes 1

androgen insensitivity syndrome (E34.5-) congenital adrenal hyperplasia (E25.0) hemolytic anemias attributable to enzyme disorders (D55.-) Marfan syndrome (Q87.4-) 5-alpha-reductase deficiency (E29.1)

Excludes 2

Ehlers-Danlos syndromes (Q79.6-)

Inherited from chapter 4Endocrine, nutritional and metabolic diseases

Excludes 1

transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Official Guidelines for E75.4

FY 2026 ›

I.C.4Chapter-specific guidanceChapter 4: Endocrine, Nutritional, and Metabolic Diseases (E00-E89)

Subsections

Find E75.4 in the alphabetic index

15 index paths lead to this code