E88.89

Other specified metabolic disorders

Risk-adjusting (HCC)Billable code

HCC risk adjustment mapping

CMS-HCC V28

HCC50

Amyloidosis, Porphyria, and Other Specified Metabolic Disorders

CMS-HCC ESRD V24

HCC23

Other Significant Endocrine and Metabolic Disorders

RxHCC V08

RXHCC43

Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders

Coding notes

Excludes 1 never coded together · Excludes 2 may co-exist

This code · E88.89
Excludes 1

adult pulmonary Langerhans cell histiocytosis (J84.82)

Synonyms

Launois-Bensaude adenolipomatosis

Inherited from E88Other and unspecified metabolic disorders
Excludes 1

histiocytosis X (chronic) (C96.6)

Use additional

codes for associated conditions

Inherited from E70-E88Metabolic disorders
Excludes 1

androgen insensitivity syndrome (E34.5-) congenital adrenal hyperplasia (E25.0) hemolytic anemias attributable to enzyme disorders (D55.-) Marfan syndrome (Q87.4-) 5-alpha-reductase deficiency (E29.1)

Excludes 2

Ehlers-Danlos syndromes (Q79.6-)

Inherited from chapter 4Endocrine, nutritional and metabolic diseases
Excludes 1

transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Official Guidelines for E88.89

FY 2026 ›

Sections that reference E88.89

Sections whose FY 2026 text names E88.89, its E88 category, or a range containing it — the chapter guidance above is the authoritative source.