E88.89
Other specified metabolic disorders
HCC risk adjustment mapping
CMS-HCC V28
Amyloidosis, Porphyria, and Other Specified Metabolic Disorders
CMS-HCC ESRD V24
Other Significant Endocrine and Metabolic Disorders
RxHCC V08
Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
Coding notes
Excludes 1 never coded together · Excludes 2 may co-exist
adult pulmonary Langerhans cell histiocytosis (J84.82)
Launois-Bensaude adenolipomatosis
histiocytosis X (chronic) (C96.6)
codes for associated conditions
transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Official Guidelines for E88.89
FY 2026 ›Subsections
Sections that reference E88.89
Sections whose FY 2026 text names E88.89, its E88 category, or a range containing it — the chapter guidance above is the authoritative source.
Find E88.89 in the alphabetic index
15 index paths lead to this code
- Adenolipomatosis, Launois-Bensaude
- Dihydropyrimidine dehydrogenase disease
- DPD
- Hoffa-Kastert disease
- Hoffa's disease
- Ketosis NEC
- Launois-Bensaude adenolipomatosis
- Liposynovitis prepatellaris
- Steatosis
- Deficiency, deficient › dihydropyrimidine dehydrogenase
- Disease, diseased › Erdheim-Chester
- Lipomatosis › Launois-Bensaude
- Syndrome › Erdheim-Chester
- Disorder › metabolism NOS › specified NEC
- Madelung's › disease › symmetrical lipomas, neck