Q40.0

Congenital hypertrophic pyloric stenosis

Risk-adjusting (HCC)Billable code

HCC risk adjustment mapping

CMS-HCC V28

HCC78

Intestinal Obstruction/Perforation

Coding notes

Excludes 1 never coded together · Excludes 2 may co-exist

This code · Q40.0

Synonyms

Congenital or infantile constriction Congenital or infantile hypertrophy Congenital or infantile spasm Congenital or infantile stenosis Congenital or infantile stricture

Inherited from chapter 17Congenital malformations, deformations and chromosomal abnormalities

Excludes 2

inborn errors of metabolism (E70-E88)

Note

Codes from this chapter are not for use on maternal records

Official Guidelines for Q40.0

FY 2026 ›

I.C.17Chapter-specific guidanceChapter 17: Congenital malformations, deformations, and chromosomal abnormalities (Q00-QA1)

Sections that reference Q40.0

IV.QEncounters for routine health screeningsOutpatient services
… Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. …

Sections whose FY 2026 text names Q40.0, its Q40 category, or a range containing it — the chapter guidance above is the authoritative source.

Find Q40.0 in the alphabetic index

12 index paths lead to this code