Q43.1

Hirschsprung's disease

Risk-adjusting (HCC)Billable code

HCC risk adjustment mapping

CMS-HCC V28

HCC78

Intestinal Obstruction/Perforation

Coding notes

Excludes 1 never coded together · Excludes 2 may co-exist

This code · Q43.1

Synonyms

Aganglionosis Congenital (aganglionic) megacolon

Inherited from chapter 17Congenital malformations, deformations and chromosomal abnormalities

Excludes 2

inborn errors of metabolism (E70-E88)

Official Guidelines for Q43.1

I.C.17Chapter-specific guidanceChapter 17: Congenital malformations, deformations, and chromosomal abnormalities (Q00-QA1)

Sections that reference Q43.1

IV.QEncounters for routine health screeningsOutpatient services
… Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. …

Sections whose FY 2026 text names Q43.1, its Q43 category, or a range containing it — the chapter guidance above is the authoritative source.

Find Q43.1 in the alphabetic index

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