Q56.1

Male pseudohermaphroditism, not elsewhere classified

Billable code

This code does not map to a risk-adjusting HCC in the loaded models.

Coding notes

Excludes 1 never coded together · Excludes 2 may co-exist

This code · Q56.1

Synonyms

46, XY with streak gonads Male pseudohermaphroditism NOS

Inherited from Q56Indeterminate sex and pseudohermaphroditism

Excludes 1

46,XX true hermaphrodite (Q99.1) androgen insensitivity syndrome (E34.5-) chimera 46,XX/46,XY true hermaphrodite (Q99.0) female pseudohermaphroditism with adrenocortical disorder (E25.-) pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99) pure gonadal dysgenesis (Q99.1)

Inherited from Q50-Q56Congenital malformations of genital organs

Excludes 1

androgen insensitivity syndrome (E34.5-) syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)

Inherited from chapter 17Congenital malformations, deformations and chromosomal abnormalities

Excludes 2

inborn errors of metabolism (E70-E88)

Note

Codes from this chapter are not for use on maternal records

Official Guidelines for Q56.1

FY 2026 ›

I.C.17Chapter-specific guidanceChapter 17: Congenital malformations, deformations, and chromosomal abnormalities (Q00-QA1)

Sections that reference Q56.1

IV.QEncounters for routine health screeningsOutpatient services
… Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. …

Sections whose FY 2026 text names Q56.1, its Q56 category, or a range containing it — the chapter guidance above is the authoritative source.

Find Q56.1 in the alphabetic index

5 index paths lead to this code