Q80-Q89
Other congenital malformations
Codes in this block
98 codes
Billableusable codeNon-billableheader / grouping codeRisk-adjusting
- Q80Congenital ichthyosisNon-billable
- Q80.0Ichthyosis vulgarisBillable
- Q80.1X-linked ichthyosisBillable
- Q80.2Lamellar ichthyosisBillable
- Q80.3Congenital bullous ichthyosiform erythrodermaBillable
- Q80.4Harlequin fetusBillable
- Q80.8Other congenital ichthyosisBillable
- Q80.9Congenital ichthyosis, unspecifiedBillable
- Q81Epidermolysis bullosaNon-billable
- Q81.0Epidermolysis bullosa simplexBillable
- Q81.1Epidermolysis bullosa letalisBillable
- Q81.2Epidermolysis bullosa dystrophicaBillable
- Q81.8Other epidermolysis bullosaBillable
- Q81.9Epidermolysis bullosa, unspecifiedBillable
- Q82Other congenital malformations of skinNon-billable
- Q82.0Hereditary lymphedemaBillable
- Q82.1Xeroderma pigmentosumBillable
- Q82.2Congenital cutaneous mastocytosisBillable
- Q82.3Incontinentia pigmentiBillable
- Q82.4Ectodermal dysplasia (anhidrotic)Billable
- Q82.5Congenital non-neoplastic nevusBillable
- Q82.6Congenital sacral dimpleBillable
- Q82.8Other specified congenital malformations of skinBillable
- Q82.9Congenital malformation of skin, unspecifiedBillable
- Q83Congenital malformations of breastNon-billable
- Q83.0Congenital absence of breast with absent nippleBillable
- Q83.1Accessory breastBillable
- Q83.2Absent nippleBillable
- Q83.3Accessory nippleBillable
- Q83.8Other congenital malformations of breastBillable
- Q83.9Congenital malformation of breast, unspecifiedBillable
- Q84Other congenital malformations of integumentNon-billable
- Q84.0Congenital alopeciaBillable
- Q84.1Congenital morphological disturbances of hair, not elsewhere classifiedBillable
- Q84.2Other congenital malformations of hairBillable
- Q84.3AnonychiaBillable
- Q84.4Congenital leukonychiaBillable
- Q84.5Enlarged and hypertrophic nailsBillable
- Q84.6Other congenital malformations of nailsBillable
- Q84.8Other specified congenital malformations of integumentBillable
- Q84.9Congenital malformation of integument, unspecifiedBillable
- Q85Phakomatoses, not elsewhere classifiedNon-billable
- Q85.0Neurofibromatosis (nonmalignant)Non-billable
- Q85.00Neurofibromatosis, unspecifiedBillable
- Q85.01Neurofibromatosis, type 1Billable
- Q85.02Neurofibromatosis, type 2Billable
- Q85.03SchwannomatosisBillable
- Q85.09Other neurofibromatosisBillable
- Q85.1Tuberous sclerosisBillable
- Q85.8Other phakomatoses, not elsewhere classifiedNon-billable
- Q85.81PTEN hamartoma tumor syndromeBillable
- Q85.82Other Cowden syndromeBillable
- Q85.83Von Hippel-Lindau syndromeBillable
- Q85.89Other phakomatoses, not elsewhere classifiedBillable
- Q85.9Phakomatosis, unspecifiedBillable
- Q86Congenital malformation syndromes due to known exogenous causes, not elsewhere classifiedNon-billable
- Q86.0Fetal alcohol syndrome (dysmorphic)Billable
- Q86.1Fetal hydantoin syndromeBillable
- Q86.2Dysmorphism due to warfarinBillable
- Q86.8Other congenital malformation syndromes due to known exogenous causesBillable
- Q87Other specified congenital malformation syndromes affecting multiple systemsNon-billable
- Q87.0Congenital malformation syndromes predominantly affecting facial appearanceBillable
- Q87.1Congenital malformation syndromes predominantly associated with short statureNon-billable
- Q87.11Prader-Willi syndromeBillable
- Q87.19Other congenital malformation syndromes predominantly associated with short statureBillable
- Q87.2Congenital malformation syndromes predominantly involving limbsBillable
- Q87.3Congenital malformation syndromes involving early overgrowthBillable
- Q87.4Marfan syndromeNon-billable
- Q87.40Marfan syndrome, unspecifiedBillable
- Q87.41Marfan syndrome with cardiovascular manifestationsNon-billable
- Q87.410Marfan syndrome with aortic dilationBillable
- Q87.418Marfan syndrome with other cardiovascular manifestationsBillable
- Q87.42Marfan syndrome with ocular manifestationsBillable
- Q87.43Marfan syndrome with skeletal manifestationBillable
- Q87.5Other congenital malformation syndromes with other skeletal changesBillable
- Q87.8Other specified congenital malformation syndromes, not elsewhere classifiedNon-billable
- Q87.81Alport syndromeBillable
- Q87.82Arterial tortuosity syndromeBillable
- Q87.83Bardet-Biedl syndromeBillable
- Q87.84Laurence-Moon syndromeBillable
- Q87.85MED13L syndromeBillable
- Q87.86Kleefstra syndromeBillable
- Q87.87Hao-Fountain SyndromeBillable
- Q87.88CTNNB1 syndromeBillable
- Q87.89Other specified congenital malformation syndromes, not elsewhere classifiedBillable
- Q89Other congenital malformations, not elsewhere classifiedNon-billable
- Q89.0Congenital absence and malformations of spleenNon-billable
- Q89.01Asplenia (congenital)Billable
- Q89.09Congenital malformations of spleenBillable
- Q89.1Congenital malformations of adrenal glandBillable
- Q89.2Congenital malformations of other endocrine glandsBillable
- Q89.3Situs inversusBillable
- Q89.4Conjoined twinsBillable
- Q89.7Multiple congenital malformations, not elsewhere classifiedBillable
- Q89.8Other specified congenital malformationsNon-billable
- Q89.81Kabuki syndromeBillable
- Q89.89Other specified congenital malformationsBillable
- Q89.9Congenital malformation, unspecifiedBillable
Official Guidelines for Q80-Q89
FY 2026 ›Sections that reference codes in Q80-Q89