Q82.2

Congenital cutaneous mastocytosis

Billable code

This code does not map to a risk-adjusting HCC in the loaded models.

Coding notes

Excludes 1 never coded together · Excludes 2 may co-exist

This code · Q82.2

Excludes 1

cutaneous mastocytosis NOS (D47.01) diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01) malignant mastocytosis (C96.2-) systemic mastocytosis (D47.02) urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)

Synonyms

Congenital diffuse cutaneous mastocytosis Congenital maculopapular cutaneous mastocytosis Congenital urticaria pigmentosa

Inherited from Q82Other congenital malformations of skin

Excludes 1

acrodermatitis enteropathica (E83.2) congenital erythropoietic porphyria (E80.0) pilonidal cyst or sinus (L05.-) Sturge-Weber (-Dimitri) syndrome (Q85.89)

Inherited from chapter 17Congenital malformations, deformations and chromosomal abnormalities

Excludes 2

inborn errors of metabolism (E70-E88)

Note

Codes from this chapter are not for use on maternal records

Official Guidelines for Q82.2

FY 2026 ›

I.C.17Chapter-specific guidanceChapter 17: Congenital malformations, deformations, and chromosomal abnormalities (Q00-QA1)

Sections that reference Q82.2

IV.QEncounters for routine health screeningsOutpatient services
… Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. …

Sections whose FY 2026 text names Q82.2, its Q82 category, or a range containing it — the chapter guidance above is the authoritative source.

Find Q82.2 in the alphabetic index

6 index paths lead to this code