E78.3
Hyperchylomicronemia
Risk-adjusting (HCC)Billable code
HCC risk adjustment mapping
RxHCC V08
RXHCC47
Disorders of Lipoid Metabolism
Coding notes
Excludes 1 never coded together · Excludes 2 may co-exist
This code · E78.3
Synonyms
Chylomicron retention disease Fredrickson's hyperlipoproteinemia, type I or V Hyperlipidemia, group D Mixed hyperglyceridemia
Inherited from E78Disorders of lipoprotein metabolism and other lipidemias
Inherited from E70-E88Metabolic disorders
Inherited from chapter 4Endocrine, nutritional and metabolic diseases
Excludes 1
transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Note
All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Official Guidelines for E78.3
FY 2026 ›Find E78.3 in the alphabetic index
18 index paths lead to this code
- Bürger-Grütz disease or syndrome
- Chylomicronemia
- Hyperchylomicronemia
- Disease, diseased › Bürger-Grütz
- Disease, diseased › chylomicron retention
- Frederickson's hyperlipoproteinemia, type › I and V
- Hepatosplenomegaly › hyperlipemic
- Hyperchylomicronemia › with hyperbetalipoproteinemia
- Hyperglyceridemia › mixed
- Lipemia › retina, retinalis
- Lipidosis › hepatosplenomegalic
- Prebetalipoproteinemia › with chylomicronemia
- Syndrome › Bürger-Grütz
- Hyperlipemia, hyperlipidemia › group › D
- Hyperlipoproteinemia › Fredrickson's type › I
- Hyperlipoproteinemia › Fredrickson's type › V
- Xanthoma › with › hyperlipoproteinemia › Type I
- Xanthoma › with › hyperlipoproteinemia › Type V