E78.6
Lipoprotein deficiency
Risk-adjusting (HCC)Billable code
HCC risk adjustment mapping
RxHCC V08
RXHCC47
Disorders of Lipoid Metabolism
Coding notes
Excludes 1 never coded together · Excludes 2 may co-exist
This code · E78.6
Synonyms
Abetalipoproteinemia Depressed HDL cholesterol High-density lipoprotein deficiency Hypoalphalipoproteinemia Hypobetalipoproteinemia (familial) Lecithin cholesterol acyltransferase deficiency Tangier disease
Inherited from E78Disorders of lipoprotein metabolism and other lipidemias
Inherited from E70-E88Metabolic disorders
Inherited from chapter 4Endocrine, nutritional and metabolic diseases
Excludes 1
transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Official Guidelines for E78.6
FY 2026 ›Find E78.6 in the alphabetic index
16 index paths lead to this code
- Abetalipoproteinemia
- Acanthocytosis
- Analphalipoproteinemia
- Bassen-Kornzweig disease or syndrome
- Hypoalphalipoproteinemia
- Hypobetalipoproteinemia
- Hypolipoproteinemia
- Tangier disease
- Deficiency, deficient › lecithin cholesterol acyltransferase
- Deficiency, deficient › lipoprotein
- Depressed › HDL cholesterol
- Disease, diseased › Tangier
- Dyslipidemia › depressed HDL cholesterol
- Disorder › glomerular › familial lecithin cholesterol acyltransferase deficiency
- Disorder › lipoprotein › deficiency
- Glomerulonephritis › in › lecithin cholesterol acyltransferase deficiency